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Learn About Desmoplastic Small Round Cell Tumor

What is the definition of Desmoplastic Small Round Cell Tumor?
Desmoplastic small round cell tumor (DSRCT) is a rare type of soft tissue cancer (sarcoma) that usually begins in the abdomen. It primarily affects children and young adults and is more common in males. It is formed by small, round cancer cells surrounded by scar-like tissue and is often found in the tissue (peritoneum) that lines the inside of the abdomen and pelvis. The tumor cells have a characteristic genetic change involving a translocation between chromosomes 11 and 22, which is important in differentiating from other similar tumors. The genetic change involved in DSRCT is acquired throughout a person's lifetime and is not inherited. Symptoms may include abdominal pain and a feeling of fullness, abdominal mass, and symptoms of gastrointestinal obstruction, such as constipation.
What are the alternative names for Desmoplastic Small Round Cell Tumor?
  • Desmoplastic small round cell tumor
  • DSRCT
  • Desmoplastic small round-cell tumor
Who are the top Desmoplastic Small Round Cell Tumor Local Doctors?
Distinguished in Desmoplastic Small Round Cell Tumor
Hematology Oncology | Oncology
Distinguished in Desmoplastic Small Round Cell Tumor
Hematology Oncology | Oncology

Kootenai Health Inc

520 N 3rd Ave, 
Sandpoint, ID 
 (46.3 mi)
Languages Spoken:
English, Latvian, Mandarin, Spanish
Accepting New Patients
Offers Telehealth

Paul White is a Hematologist Oncology specialist and an Oncologist in Sandpoint, Idaho. Dr. White and is rated as a Distinguished provider by MediFind in the treatment of Desmoplastic Small Round Cell Tumor. His top areas of expertise are Desmoplastic Small Round Cell Tumor, Philadelphia-Negative Chronic Myeloid Leukemia, Chronic Myelogenous Leukemia (CML), Familial Pancreatic Cancer, and Bone Marrow Transplant. Dr. White is currently accepting new patients.

Experienced in Desmoplastic Small Round Cell Tumor
Oncology | Geriatrics
Experienced in Desmoplastic Small Round Cell Tumor
Oncology | Geriatrics

Kalispell Regional Medical Center Inc

298 Osloski Rd, 
Eureka, MT 
 (41.4 mi)
Languages Spoken:
English, Portuguese
Accepting New Patients
Offers Telehealth

Jose Ness is an Oncologist and a Geriatrics provider in Eureka, Montana. Dr. Ness and is rated as an Experienced provider by MediFind in the treatment of Desmoplastic Small Round Cell Tumor. His top areas of expertise are Paget Disease of the Breast, Lymphofollicular Hyperplasia, Chronic Lymphocytic Leukemia (CLL), and Richter Syndrome. Dr. Ness is currently accepting new patients.

 
 
 
 
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Advanced in Desmoplastic Small Round Cell Tumor
Hematology Oncology | Hematology | Oncology
Advanced in Desmoplastic Small Round Cell Tumor
Hematology Oncology | Hematology | Oncology

American Oncology Partners PA

13424 E Mission Ave, Suite A, 
Spokane Valley, WA 
 (91.6 mi)
Languages Spoken:
English, Italian, Romanian, Russian, Spanish, Swedish
Accepting New Patients
Offers Telehealth

Arvind Chaudhry is a Hematologist Oncology specialist and a Hematologist in Spokane Valley, Washington. Dr. Chaudhry and is rated as an Advanced provider by MediFind in the treatment of Desmoplastic Small Round Cell Tumor. His top areas of expertise are Chronic Lymphocytic Leukemia (CLL), Lung Cancer, Paget Disease of the Breast, Pleuropulmonary Blastoma, and Bone Marrow Aspiration. Dr. Chaudhry is currently accepting new patients.

What are the latest Desmoplastic Small Round Cell Tumor Clinical Trials?
Safety and Efficacy of CAR-T Cell Therapy for Relapsed/refractory Neuroblastoma and Desmoplastic Small Round Cell Tumors: a Single-arm, Open-label Trial.

Aims: 1. To evaluate the safety and efficacy of GD2/B7H3 CAR-T therapy for relapsed/refractory neuroblastoma, and observe its pharmacokinetic/pharmacodynamic characteristics and the survival of CAR-T cells in relapsed/refractory neuroblastoma patients. 2. To evaluate the safety and efficacy of GD2/B7H3 CAR-T therapy for relapsed/refractory desmoplastic small round cell tumor, and observe its pharmacokin...

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Lurbinectedin in FET-Fusion Tumors (LIFFT)

Summary: The purpose of this study is to find out if a drug called lurbinectedin (the study drug) is safe and effective at treating people with recurrent or relapsed solid tumors, including Ewing sarcoma.

Who are the sources who wrote this article ?

Published Date: May 02, 2022
Published By: Genetic and Rare Diseases Informnation Center

What are the Latest Advances for Desmoplastic Small Round Cell Tumor?
Variant Pseudocystic Desmoplastic Small Round Cell Tumor With Heterologous Mullerian Cysts.
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