Gerstmann-Straussler-Scheinker Syndrome Overview

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Learn About Gerstmann-Straussler-Scheinker Syndrome

What is the definition of Gerstmann-Straussler-Scheinker Syndrome?
Gerstmann-Straussler-Scheinker disease (GSS) is a type of prion disease. Prion diseases are a group of conditions that affect the nervous system. The main feature of GSS is a progressive degeneration of the cerebellum (a part of the brain that controls coordination, balance, equilibrium and muscle tone), as well as different degrees of dementia. It is caused by changes in the PRNP gene and inheritance is autosomal dominant.
What are the alternative names for Gerstmann-Straussler-Scheinker Syndrome?
  • Gerstmann-Straussler-Scheinker disease
  • Amyloidosis cerebral with spongiform encephalopathy
  • Cerebellar ataxia, progressive dementia, and amyloid deposits in the central nervous system
  • Encephalopathy subacute spongiform Gerstmann-Straussler type
  • GSSD
  • Gerstmann Straussler Scheinker syndrome
  • Gerstmann-Straussler-Scheinker syndrome
  • Subacute spongiform encephalopathy, Gerstmann-Straussler type
Who are the top Gerstmann-Straussler-Scheinker Syndrome Local Doctors?
Dr. Rebecca E. Sell
Pulmonary Medicine
Dr. Rebecca E. Sell
Pulmonary Medicine

The Association Of University Physicians

1959 Ne Pacific St, 
Seattle, WA 
 (180.3 mi)
206-598-4333
Languages Spoken:
English, Hindi, Punjabi, Spanish
See accepted insurances
Accepting New Patients
Offers Telehealth

Rebecca Sell is a Pulmonary Medicine provider in Seattle, Washington. Dr. Sell and is rated as an Experienced provider by MediFind in the treatment of Gerstmann-Straussler-Scheinker Syndrome. Her top areas of expertise are Empyema, Pneumonia, Gerstmann-Straussler-Scheinker Syndrome, Acute Respiratory Distress Syndrome (ARDS), and Gastrostomy. Dr. Sell is currently accepting new patients.

Dr. Erik V. Soloff
Radiology
Dr. Erik V. Soloff
Radiology

The Association Of University Physicians

1959 Ne Pacific St, 
Seattle, WA 
 (180.3 mi)
206-598-4333
Languages Spoken:
English, American Sign Language, Sign Language
See accepted insurances
Accepting New Patients
Offers Telehealth

Erik Soloff is a Radiologist in Seattle, Washington. Dr. Soloff and is rated as an Experienced provider by MediFind in the treatment of Gerstmann-Straussler-Scheinker Syndrome. His top areas of expertise are Pancreatic Ductal Adenocarcinoma, Mesothelioma, Fibrolamellar Carcinoma, and Cholangiocarcinoma (Bile Duct Cancer). Dr. Soloff is currently accepting new patients.

 
 
 
 
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Published Date: May 02, 2022
Published By: Genetic and Rare Diseases Informnation Center