Syringomyelia Overview
Learn About Syringomyelia
Syringomyelia is a cyst-like collection of cerebrospinal fluid (CSF) that forms in the spinal cord. Over time, it may damage the spinal cord.
Syrinx
The fluid-filled cyst is called a syrinx. The spinal fluid buildup may be caused by:
- Birth defects (especially Chiari malformation, in which part of the brain pushes down onto the spinal cord at the base of the skull)
- Spinal cord trauma
- Tumors of the spinal cord
The fluid-filled cyst usually begins in the neck area. It expands slowly, putting pressure on the spinal cord and slowly causing damage.
Onset of syringomyelia is usually between 25 to 40 years old. Males are more affected than females.
If the condition is due to birth defects, there may be no symptoms until age 30 to 40 years. Symptoms of syringomyelia usually appear slowly and worsen over many years. In the case of trauma, the onset of symptoms may be as early as 2 to 3 months of age. If there are symptoms, they may include:
- Headache
- Scoliosis (in children)
- Loss of muscle mass (wasting, atrophy), often in the arms and hands
- Loss of reflexes in upper limbs
- Increased reflexes in lower limbs
- Spasms or tightness in the leg or hand and arm muscles
- Muscle function loss, loss of ability to use arms or legs
- Numbness that decreases the feeling of pain or temperature; lowers the ability to feel when the skin is being touched; occurs in the neck, shoulders, upper arms, and trunk in a cape-like pattern; and slowly gets worse over time
- Pain down the arms, neck, or into the middle back or legs
- Weakness (decreased muscle strength) in the arms or legs
- Painless burn or injury of the hand
- Difficulty walking or toe walking in children
- Uncontrollable movements of the eyes (nystagmus)
- Condition that affects the nerves to the eye and face (Horner syndrome)
- Trouble controlling the bowel or bladder
There is no known effective treatment for syringomyelia. The goals of treatment are to stop the spinal cord damage from getting worse and to improve function.
Medicines and devices can help with pain.
Surgery may be needed to relieve pressure in the spinal cord. Physical and occupational therapy may be needed to improve muscle function and help maximize independence.
Ventriculoperitoneal shunting or syringosubarachnoid shunting may be needed. This is a procedure in which a catheter (thin, flexible tube) is inserted to drain the fluid buildup.
Other treatments are available to manage bowel and bladder problems and spasticity.
David Robirds is an Internal Medicine provider in Greenville, South Carolina. Dr. Robirds and is rated as an Experienced provider by MediFind in the treatment of Syringomyelia. His top areas of expertise are Glucocorticoid-Remediable Aldosteronism, Familial Hypertension, Hypertension, and End-Stage Renal Disease (ESRD). Dr. Robirds is currently accepting new patients.
Partnermd South Carolina PC
William Messer is a Family Medicine provider in Greenville, South Carolina. Dr. Messer and is rated as an Experienced provider by MediFind in the treatment of Syringomyelia. His top areas of expertise are Type 2 Diabetes (T2D), Glucocorticoid-Remediable Aldosteronism, Familial Hypertension, and Hypertension. Dr. Messer is currently accepting new patients.
Bon Secours Medical Group Greenville Specialty Care LLC
Adam Mathes is a Neurosurgery provider in Greenville, South Carolina. Dr. Mathes and is rated as an Experienced provider by MediFind in the treatment of Syringomyelia. His top areas of expertise are Spinal Stenosis, Subdural Hematoma, Chronic Subdural Hematoma, Cervical Disc Surgery, and Herniated Disc Surgery. Dr. Mathes is currently accepting new patients.
Without treatment, the disorder may get worse very slowly. Over time, it may cause severe disability.
Surgery usually stops the condition from getting worse. Nervous system function will improve in about 30% of the people who have surgery.
Without treatment, the condition may lead to:
- Loss of nervous system function
- Permanent disability
Possible complications of surgery include:
- Infection
- Other complications of surgery
Contact your provider if you have symptoms of syringomyelia.
There is no known way to prevent this condition, other than avoiding injuries to the spinal cord. Getting treated right away slows the worsening due to this disorder.
Summary: A global analysis of craniospinal hemodynamics and hydrodynamics is necessary to better understand the pathophysiology of Chiari malformations. This includes an analysis of intraventricular CSF flow, intracranial subarachnoid spaces, foramen magnum, cervical subarachnoid spaces and within the syringomyelia cavity when present. The investigators will also analyze the pulsatility of the cerebellar t...
Summary: To determine whether Subarachnoid-Subarachnoid (S-S) Bypass results in better patient outcomes with fewer complications and improved quality of life compared to intradural adhesion lysis in individuals with Spinal Arachnoiditis and Syringomyelia.
Published Date: June 13, 2024
Published By: Joseph V. Campellone, MD, Department of Neurology, Cooper Medical School at Rowan University, Camden, NJ. Review provided by VeriMed Healthcare Network. Also reviewed by David C. Dugdale, MD, Medical Director, Brenda Conaway, Editorial Director, and the A.D.A.M. Editorial team.
Alobeidi F, Thurnher MM, Jäger HR. Non-tumoural spinal cord lesions. In: Adam A, Dixon AK, Gillard JH, Schaefer-Prokop CM, eds. Grainger & Allison's Diagnostic Radiology. 7th ed. Philadelphia, PA: Elsevier; 2021:chap 50.
Benglis DM, Jea A, Vanni S, Shah AH, Green BA. Syringomyelia. In: Garfin SR, Eismont FJ, Bell GR, Fischgrund JS, Bono CM, eds. Rothman-Simeone and Herkowitz's The Spine. 7th ed. Philadelphia, PA: Elsevier; 2018:chap 94.
National Institute of Neurological Disorders and Stroke website. Syringomyelia. www.ninds.nih.gov/health-information/disorders/syringomyelia. Reviewed September 23, 2023. Accessed July 3, 2024.
Roguski M, Groves ML. Adult syringomyelia. In: Winn HR, ed. Youmans and Winn Neurological Surgery. 8th ed. Philadelphia, PA: Elsevier; 2023:chap 334.